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Figure 2 | Molecular Medicine

Figure 2

From: Interstitial Lung Disease and Pulmonary Fibrosis in Hermansky-Pudlak Syndrome Type 2, an Adaptor Protein-3 Complex Disease

Figure 2

Representative computed tomography scan images from two children with HPS-2 and severe interstitial lung disease. (A) shows severe bilateral ground glass opacities, thickening of interlobular septa and pulmonary fibrosis at the level of the carina for subject 1 at 8 years of age. A computed tomography scan image at the same level shows mild improvement in infiltrates (arrows) at 14 years of age (B). (C) shows extensive bilateral ground glass opacities when subject 4 was 4 years of age. A coronal CT scan image demonstrates diffuse ground glass infiltrates and interstitial reticulations (open arrows) in subject 4 (D).

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