Skip to main content

Table 2 Pulmonary function testing and blood cytokine concentrations.

From: Interstitial Lung Disease and Pulmonary Fibrosis in Hermansky-Pudlak Syndrome Type 2, an Adaptor Protein-3 Complex Disease

 

Age (years)

FEV1a

FVCa

FEV1/FVCb

TLCc

DLCOc

 

TGF-β1 (ng/mL)

IL-17A (pg/mL)

Subject 1

8

42 (0.39)

40 (0.39)

100

88

NA

NA

170.6

8.8

 

14

65 (0.94)

71 (1.09)

86

109

29

10.1

36

2.6

Subject 2

25

87 (3.65)

90 (4.70)

78

87

105

NA

39.1

3.7

 

27

85 (3.49)

90 (4.62)

75

94

96

NA

72

4

Subject 3

20

82 (3.54)

90 (3.70)

74

91

84

NA

74.8

0

 

22

87 (4.79)

90 (4.72)

78

94

108

NA

30.7

0

  1. NA, not available.
  2. aPercentage of predicted values (actual values, liters).
  3. bPercentage.
  4. cPercentage of predicted values.
  5. dNO, exhaled nitric oxide (at 50 mL/sec), parts per billion (normal range, <15 to 25 parts per billion).
Back to article page

Molecular Medicine

ISSN: 1528-3658