Table 1 Distribution of CLN3 patients according to slow, average or rapid disease progression defined by the Index of Relative Severity.
From: Analysis of Potential Biomarkers and Modifier Genes Affecting the Clinical Course of CLN3 Disease
Clinical course | Index of Relative Severity | Number of patients |
|---|---|---|
Slow | >+0.5 | 5 |
Average | −0.5 to +0.5 | 9 |
Rapid | <−0.5 | 11 |